Klippel Trenaunay Weber Syndrome:
Klippel-Trenaunay syndrome is characterized by a triad of port-wine stain, varicose
veins, and bony and soft tissue hypertrophy involving an extremity. KTWS generally
affects a single extremity, although cases of multiple affected limbs have been
reported. The leg is the most common site followed by the arms, the trunk, and
rarely the head and the neck. This hemangioma has a distinct, linear border
that respects the midline. Hemangioma is often noted on the lateral aspect of
the limb.It is typically of the nevus flammeus type, but cavernous hemangiomas
or lymphangiomas may also occur. Nevus flammeus is a salmon pink patch, sometimes
with a verrucous quality, which evolves to a deep purple color with time. Unlike
strawberry hemangiomas, the port-wine stain hemangioma possesses neither a proliferative
nor a regressing phase.


