Kassabach-Merritt Syndrome:

Kassabach-Merrit (KM) syndrome is a consumption coagulopathy that occurs as a complication of angiomatous nevi. Angiomatous nevi leading to KM syndrome are generally single, deep lesions of large size, but the disorder can vary occasionally and occur in association with smaller and more superficial lesions. The responsible angiomas most commonly occur on the trunk, neck and proximal parts of the limbs, particularly the thighs and shoulders, and are relatively uncommon on the head. This picture is of an 2 month old infant who was brought to the pediatric outpatient department for evaluation of a swollen left arm since birth. On examination the limb was enveloped by a rapidly growing hemangioma. Although the child appeared well and the hemangioma was not symptomatic, a small ulcer was noted near the elbow, and the platelet count was less than 10,000.